Guide To Treating Maple Syrup Urine Disease

Intravenous Treatment

A patient with maple syrup urine disease is constantly at risk of a metabolic crisis, even if they follow a strict diet. A metabolic crisis occurs when the amino acid levels in the blood get too high. Patients must be treated with emergency medical intervention to lower their amino acid levels, particularly their levels of leucine. Some medical professionals recommend aggressive medical therapy to protect against and during metabolic crises.

The goal of this therapy is to reduce the factors causing the crisis. One way to do this is by increasing the calories an individual ingests. Any method of doing so is deemed valid. A patient may have intravenous treatment with glucose. If a doctor deems it necessary, there may also be a glucose-insulin drip added to the treatment plan.